M34.1 CR(E)ST syndrome
Instructional Notes:
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M34.1
Description: CR(E)ST syndrome
Inclusion Term:
- Combination of calcinosis, Raynaud's phenomenon, esophageal dysfunction, sclerodactyly, telangiectasia
↓
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M34
Description: Systemic sclerosis [scleroderma]
Exclude1:
- circumscribed scleroderma (L94.0)
- neonatal scleroderma (P83.88)
↓
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M30-M36
Description: Systemic connective tissue disorders (M30-M36)
Exclude1:
- autoimmune disease, single organ or single cell-type -code to relevant condition category
Include:
- autoimmune disease NOS
- collagen (vascular) disease NOS
- systemic autoimmune disease
- systemic collagen (vascular) disease
↓
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M00-M99
Description: Diseases of the musculoskeletal system and connective tissue
Exclude2:
- arthropathic psoriasis (L40.5-)
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- compartment syndrome (traumatic) (T79.A-)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Notes:
- Use an external cause code following the code for the musculoskeletal condition, if applicable, to identify the cause of the musculoskeletal condition